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Journal of the Korean Society of Pediatric Nephrology 2013;17(2): 73-78. doi: https://doi.org/10.3339/jkspn.2013.17.2.73
소아 및 성인 마제신 환자들의 임상적 특징과 비교
김유경1, 권남희1, 강동일*, 정우영1
1인제대학교 의과대학 부산백병원 소아청소년과
2인제대학교 의과대학 부산백병원 비뇨기과학교실*
Clinical Manifestations and Characteristics in Patients with Horseshoe Kidney
Yu Kyong Kim1, Nam Hee Kwon1, Dong Il Kang*, Woo Yeong Chung1
1Department of Pediatrics, Busan Paik Hospital, Inje University, Busan, Korea
2Department of Urology*, Busan Paik Hospital, Inje University, Busan, Korea
Corresponding Author: Woo Yeong Chung ,Tel: 051-890-6280, Fax: 051-896-4515, Email: chungwy@chol.com
Received: August 8, 2013;  Accepted: October 4, 2013.
This is an open-access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http:// creativecommons. org/licenses/bync/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
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ABSTRACT
Purpose: We aimed to investigate the clinical characteristics and associated diseases in children with a horseshoe kidney and compared these data between children and adults.

Method :
We performed a retrospective analysis of the medical records and radiological findings of 43 patients diagnosed with a horseshoe kidney in the Busan Paik Hospital. The subjects were divided into the children’s group (14 cases, age <18 years) and the adult group (29 cases, age ≥18 years).

Results :
The study group consisted of 17 males and 26 females with a median age of 34 years. In the children’s group (14 cases), 5 subjects were male and 9 were female, with a mean age of 6.7±6.2 years. Most of the subjects were asymptomatic and were incidentally diagnosed with horseshoe kidney during their evaluation for another disease. Among the associated diseases in the children’s group, Turner syndrome was the most common (5 cases), whereas ureteropelvic junction (UPJ) stricture was observed in 2 cases (14.2%). None of the children exhibited abnormal renal function during the follow-up period. In the adult group (29 cases), 12 subjects were male and 17 were female, with a mean age of 48 years. Eighteen patients were incidentally diagnosed with horseshoe kidney during their evaluation for another disease, and 11 patients had hematuria or abdominal pain due to renal stones. Among the associated diseases in the adult group, Turner syndrome was the most common (5 cases), and UPJ stricture was observed in 5 cases; the other accompanying diseases included hydronephrosis and overactive bladder. Six patients exhibited decreased renal function (serum creatinine level >1.5) during the follow-up period.

Conclusion :
Horseshoe kidney is usually diagnosed incidentally in both children and adults. In the present study, we noted that Turner syndrome was the most common associated disease in children. In addition, most children were asymptomatic but had a high risk of urologic complications after the transition to adulthood. Therefore, children with horseshoe kidney require continuous follow-up.
Key words: Horseshoe kidney | Children | Turner syndrome | Urogenital abnormalities | Urinary stones
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