Nutcracker Syndrome in Siblings

Lee, Na-Ra; Oh, Jung-Min; Yim, Hyung-Eun; Yoo, Kee-Hwan; Hong, Young-Sook; Lee, Joo-Won

doi:2010.14.2.240

J Korean Soc Pediatr Nephrol > Volume 14(2); 2010 > Article

J Korean Soc Pediatr Nephrol 2010;14(2): 240-245. doi: https://doi.org/10.3339/jkspn.2010.14.2.240

형제에서 발생한 호두까기 증후군 증례보고 및 문헌 고찰

이나라, 오정민, 임형은, 유기환, 홍영숙, 이주원

¹고려대학교 의과대학 소아과학교실
²고려대학교 의과대학 소아과학교실
³고려대학교 의과대학 소아과학교실
⁴고려대학교 의과대학 소아과학교실
⁵고려대학교 의과대학 소아과학교실
⁶고려대학교 의과대학 소아과학교실

Nutcracker Syndrome in Siblings

Na-Ra Lee, Jung-Min Oh, Hyung-Eun Yim, Kee-Hwan Yoo, Young-Sook Hong, Joo-Won Lee

¹Department of Pediatrics, College of Medicine, Korea University
²Department of Pediatrics, College of Medicine, Korea University
³Department of Pediatrics, College of Medicine, Korea University
⁴Department of Pediatrics, College of Medicine, Korea University
⁵Department of Pediatrics, College of Medicine, Korea University
⁶Department of Pediatrics, College of Medicine, Korea University

Received: September 14, 2010; Revised: October 13, 2010. Accepted: October 18, 2010.

ABSTRACT

Nutcracker syndrome refers to the compression of the left renal vein between the abdominal aorta and superior mesenteric artery which can lead to renal vein hypertension. Patients can present with hematuria, proteinuria, dysuria or abdominal pain. In diagnosing the nutcracker syndrome, measurement of the peak velocity ratio of aorto-mesenteric border versus renal hilum by Doppler sonography is useful. Currently, there are few reports about the genetic correlation in this syndrome. We report two cases of the nutcracker syndrome found in male siblings with hematuria.

Key words: Nutcracker syndrome | Hematuria | Children