A Case of Nephrotic Syndrome in Behcet Syndrome

Juhng, Woo-Suk; Kim, Hye-Young; Lee, Dae-Yeol

J Korean Soc Pediatr Nephrol > Volume 2(1); 1998 > Article

Journal of the Korean Society of Pediatric Nephrology 1998;2(1): 73-76.

신 증후군을 동반한 베체트 증후군(Behcet syndrome) 1례

정우석, 김혜영, 이대열

¹전북대학교 의과대학 소아과학교실
²전북대학교 의과대학 소아과학교실
³전북대학교 의과대학 소아과학교실

A Case of Nephrotic Syndrome in Behcet Syndrome

Woo-Suk Juhng, Hye-Young Kim, Dae-Yeol Lee

¹Department of Pediatrics, Chonbuk National University, Medical School
²Department of Pediatrics, Chonbuk National University, Medical School
³Department of Pediatrics, Chonbuk National University, Medical School

ABSTRACT

Behcet syndrome is a multisystem disease complex of unknown cause. It is usually manifested by aphthous oral and genital ulcers, uveitis and skin eruption. Less frequently, CNS involvement, colitis, large vessel vasculitis, and myocarditis occur. Recently, several studies have reported renal manifestations of amyloidosis and focal necrotizing glomerulonephritis in Behcet syndrome. We describe a patient with Behcet syndrome who experienced nephrotic syndrome with focal effacement of epithelial foot process in glomeruli. A brief review of literature ensues.

Key words: Nephrotic syndrome | Behcet syndrome