국소성 분절성 사구체 경화증에 의한 영아형 신증후군 1례 |
김세은, 한영심, 송민섭, 정우영 |
1인제대학교 의과대학 부산백병원 소아과학교실 2인제대학교 의과대학 부산백병원 소아과학교실 3인제대학교 의과대학 부산백병원 소아과학교실 4인제대학교 의과대학 부산백병원 소아과학교실 |
A Case of Infantile Nephrotic Syndrome with Focal Segmental Glomerulosclerosis |
Se Eun Kim, Young Sim Han, Min Seop Song, Woo Yeong Chung |
1Department of Pediatrics, Pusan Paik Hospital, Inje University, College of Medicine 2Department of Pediatrics, Pusan Paik Hospital, Inje University, College of Medicine 3Department of Pediatrics, Pusan Paik Hospital, Inje University, College of Medicine 4Department of Pediatrics, Pusan Paik Hospital, Inje University, College of Medicine |
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ABSTRACT |
Focal Segmental Glomerulosclerosis(FSGS) is one of the underlying pathology of congenital and infantile nephrotic syndrome. There is no ultimate curative treatment except renal transplantation. We have experienced a case of infantile nephrotic syndrome In a 10 month old boy who presented with proteinuria and hematuria. His elder brother also suffered from nephrotic syndrome and died at the age of 18 months due to sepsis. We have diagnosed this patient with clinical manifestations, laboratory data and pathologic findings which was done by open renal biopsy. The patient expired 54 days after admission because or progressive uremia and sepsis. |
Key words:
Infantile Nephrotic Syndrome | Focal Segmental Glomerulosclerosis |
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