A Case of Renovascular Hypertension Due to Renal Artey Stenosis Related to Moyamoya Disease

Kim, Joung-A; Kim, Seung; Kim, Hyo-Sun; Shin, Jae-Il; Jeong, Il-Cheon; Kim, Dong-Seok; Kim, Myung-Joon; Lee, Do-Yun; Lee, Jae-Seung

doi:2007.11.2.294

J Korean Soc Pediatr Nephrol > Volume 11(2); 2007 > Article

J Korean Soc Pediatr Nephrol 2007;11(2): 294-298. doi: https://doi.org/10.3339/jkspn.2007.11.2.294

모야모야병과 동반된 신 동맥 협착에 따른 신성 고혈압을 보인 1례

김정아, 김승, 김효선, 신재일, 정일천, 김동석, 김명준, 이도연, 이재승

¹연세대학교 의과대학 소아과학교실, 신장질환 연구소
²연세대학교 의과대학 소아과학교실, 신장질환 연구소
³연세대학교 의과대학 소아과학교실, 신장질환 연구소
⁴연세대학교 의과대학 소아과학교실, 신장질환 연구소
⁵연세대학교 의과대학 소아과학교실, 신장질환 연구소
⁶연세대학교 의과대학 신경외과학교실
⁷연세대학교 의과대학 진단방사선과학교실
⁸연세대학교 의과대학 진단방사선과학교실
⁹연세대학교 의과대학 소아과학교실, 신장질환 연구소

A Case of Renovascular Hypertension Due to Renal Artey Stenosis Related to Moyamoya Disease

Joung-A Kim, Seung Kim, Hyo-Sun Kim, Jae-Il Shin, Il-Cheon Jeong, Dong-Seok Kim, Myung-Joon Kim, Do-Yun Lee, Jae-Seung Lee

¹Department of Pediatrics, The Institute of Kidney Disease Yonei University College of Medicine
²Department of Pediatrics, The Institute of Kidney Disease Yonei University College of Medicine
³Department of Pediatrics, The Institute of Kidney Disease Yonei University College of Medicine
⁴Department of Pediatrics, The Institute of Kidney Disease Yonei University College of Medicine
⁵Department of Pediatrics, The Institute of Kidney Disease Yonei University College of Medicine
⁶Department of Neurosurgery, Yonsei University College of Medicine
⁷Department of Radiology, Yonsei University College of Medicine
⁸Department of Radiology, Yonsei University College of Medicine
⁹Department of Pediatrics, The Institute of Kidney Disease Yonei University College of Medicine

ABSTRACT

Moyamoya disease is a progressive cerebrovascular disorder with stenosis or occlusion of the bilateral internal carotid arteries with abnormal vascular networks at the base of the brain. Previous reports have shown that there are extracranial vascular involvements in Moyamoya disease, especially in the renal artery. We report a 7-year-old patient with Moyamoya disease associated with renovascular hyper tension, who presented in infancy with seizures and hemiparesis. Renal angiography showed multiple stenoses of the right renal artery. Although renal artery stenosis in Moyamoya disease has been effectively treated with balloon angioplasty, stent implantation, or surgery, bat-loon angioplasty could not be done in this patient due to multiple stenoses. His blood pressure was successfully controlled with medical treatment, and remained normotensive during the follow up period of 6 months.

Key words: Moyamoya disease | Renovascular hypertension | Renal angiogram