J Korean Soc Pediatr Nephrol > Volume 1(2); 1997 > Article
J Korean Soc Pediatr Nephrol 1997;1(2): 144-150.
소아의 낭포성 신질환
이지숙, 노광식, 김지홍, 이재승, 김병길
1연세대학교 의과대학 소아과학교실
2연세대학교 의과대학 소아과학교실
3연세대학교 의과대학 소아과학교실
4연세대학교 의과대학 소아과학교실
5연세대학교 의과대학 소아과학교실
Cystic Diseases of the Kidney in Children
Ji-Suk Lee, Kwang-Sik Rho, Ji-Hong Kim, Jae-Seung Lee, Pyung-Kil Kim
1Department of Pediatrics, Yonsei University, Collage of Medicine
2Department of Pediatrics, Yonsei University, Collage of Medicine
3Department of Pediatrics, Yonsei University, Collage of Medicine
4Department of Pediatrics, Yonsei University, Collage of Medicine
5Department of Pediatrics, Yonsei University, Collage of Medicine
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ABSTRACT
Purpose : The kidney is one of the most common sites of cyst formation. Cystic diseases of the kidney are a diverse group of clinicopathologic entities and variable prognosis. They span a wide range of both age of presentation and severity of the renal disease. And many of them are systemic disorders, sharing similar process of cyst formation in other organs. Recently, development of imaging studies has been contributing widely to the diagnosis of the diseases. Treatment, however, is not established satisfactorily. We performed this study to evaluate the occurrence and treatment of cystic diseases of the kidney.
Methods : We reviewed retrospectively the medical records of 44 patients with cystic diseases of the kidney in the Department of Pediatrics, during last 11 years.
Results : In the 44 patients with cystic diseases of the kidney, 31 patients(71%) had multicystic dysplastic kidney and 11(35%) of them received nephrectomy due to differentiation from neoplasms or severe abdominal distension. Seven patients(16%) had polycystic kidney disease, and all of them were infantile type. Five patients(11%) were diagnosed as having a simple renal cysts. Progression to renal failure was noted in none of the cases. In 14(32%) out of total 44 patients, the diagnosis was made in neonatal or infantile pelted.
Conclusion : The incidence of cystic diseases of the kidney appeared very low, but further investigation on their pathogenesis, classification, and indication of treatment is needed.
Key words: Kidney | Cystic disease

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